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amyotrophic lateral sclerosis (ALS) - Coggle Diagram
amyotrophic lateral sclerosis (ALS)
pathophysiology
atrophy of muscles
progressive loss of movement in hands, arms, legs
loss of muscle function in face & chest
loss of motor function causes quadriplegia
signs
muscle atrophy
slurred speach
tripping or falling
symptoms
difficulty chewing or swallowing
stiff muscles
muscle weakness
diagnosis
electromyogram
nerve conduction study
muscle or nerve biopsy
treatment
medication: riluzole, edaravone, tofersen
physical therapy
breathing care
nutrional support
prognosis
average survival time after diagnosis is 3 years
symptoms get worse over time
etiology
cause unknown
genetic & viral immune factors have been suggested