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Ninja Nerd Pulmonary Hypertension - Coggle Diagram
Ninja Nerd Pulmonary Hypertension
Definition
A mean pulmonary arterial pressure
≥20 mmHg.
Types
Type 1
Idiopathic
Type 2
Type 3
Type 5
Type 4
PLATE
P (group 1): Pulmonary artery hypertension
L (group 2): Left heart disease
A (group 2): Airway disease (chronic lung disease and/or hypoxaemia)
T (group 4): Thromboembolic disease (or other obstructive conditions)
E (group 5): Everything else (anything unclear or multifactorial)
Type 1
Pathophysiology
BMPR 2 gene mutation
↑ Vasoconstrictors (endothelin)
↓ Vasodilators (NO, PGI2)
↑ Pulmonary vaso-constriction
↑ Pumonary vascular resistance / pulmonary artery pressure
Pulmonary hypertension
Aetiology
Iodiopathic
BMPR2 mutation
Type 2
Aetiology
Left heart failure
Pathophysiology
Left heart failur
↓ Cardiac output
LV End diastolic pressure increases
Backflow of blood into pulmonary veins
Increased pulmonary capillary wedge pressure