Epidermolysis bullsa dystrophic

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Symptoms Screenshot_20231021_230230_Chrome

Symptoms of epidermolysis bullosa include:

Thinning of the skin, making it ulcerate easily, especially on the hands and feet

The appearance of ulcers inside the mouth and throat

Scalp sores and hair loss (cicatricial alopecia)

Thinning of the skin

Difficulty swallowing

Screenshot_20231021_230422_Google

Epidermolysis bullosa is a rare disease that causes fragility and ulceration of the skin. The skin may develop blisters when exposed to minor injury, even from heat, friction, or scratching. In severe cases, blisters may appear inside the body, such as the lining of the mouth or stomach. Epidermolysis bullosa is a hereditary disease that usually occurs in infants or young children :

Definitio Screenshot_20231021_230325_Google

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pharmaceutical

Surgical intervention may be necessary. Options sometimes used for this condition include:

Placement of a feeding tube. To improve nutrition and help with weight gain, a feeding tube (gastric tube) may be needed to deliver food directly to the stomach.

Skin grafts. If scarring affects the function of one hand, your surgeon may suggest skin grafts.

Complications

Infection. Blistered skin can become infected with bacteria

Bloodstream infection. Sepsis occurs when bacteria resulting from an infection enter the bloodstream and spread throughout the body. Sepsis can spread quickly and cause shock and organ failure.

Fingers and joint changes. Severe cases of epidermolysis bullosa can cause the fingers or toes to fuse, causing abnormal curvature of the joints (contractures). This can affect the functions of the fingers, knees and elbows.

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