Epidermolysis bullsa dystrophic
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Symptoms
Symptoms of epidermolysis bullosa include:
Thinning of the skin, making it ulcerate easily, especially on the hands and feet
The appearance of ulcers inside the mouth and throat
Scalp sores and hair loss (cicatricial alopecia)
Thinning of the skin
Difficulty swallowing
Epidermolysis bullosa is a rare disease that causes fragility and ulceration of the skin. The skin may develop blisters when exposed to minor injury, even from heat, friction, or scratching. In severe cases, blisters may appear inside the body, such as the lining of the mouth or stomach. Epidermolysis bullosa is a hereditary disease that usually occurs in infants or young children :
Definitio
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pharmaceutical
Surgical intervention may be necessary. Options sometimes used for this condition include:
Placement of a feeding tube. To improve nutrition and help with weight gain, a feeding tube (gastric tube) may be needed to deliver food directly to the stomach.
Skin grafts. If scarring affects the function of one hand, your surgeon may suggest skin grafts.
Complications
Infection. Blistered skin can become infected with bacteria
Bloodstream infection. Sepsis occurs when bacteria resulting from an infection enter the bloodstream and spread throughout the body. Sepsis can spread quickly and cause shock and organ failure.
Fingers and joint changes. Severe cases of epidermolysis bullosa can cause the fingers or toes to fuse, causing abnormal curvature of the joints (contractures). This can affect the functions of the fingers, knees and elbows.
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