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HLH - Coggle Diagram
HLH
Pathophysiology
Macrophages
IL1, IL6, IL18
GM-CSF / IFN gamma
CD 8+
Primary
Peadiatric
Secondary
Triggering event
Risk factors
Genetics
Background inflammation
Immune suppression
Infection
Herpes
EBV
TV
CMV
Malignancy
Lymphoma
Clinical
Triad
Refractory fever
Low WCC, Low platelets
Organomegaly
Hyperinflammation
Ferritin
d-dimer
CRP
H-Score
169
Accurate to 90%
9 criteria
Management
Etoposide
Anakira
Tocilizumab
Dexamethasone
JAK inhibitors
alemtuzumab
Definition
Haemophagocytic Lympho-Histocytosis
Hyperinflammation