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CYSTIC FIBROSIS 20210522_171940 - Coggle Diagram
CYSTIC FIBROSIS
DEFINATION
An inherited life-threatening disorder that damages the lungs and digestive system
CLINICAL MANIFESTATIONS
Frequent lung infections
Infertility, especially in men
Wheezing or trouble breathing
Trouble growing or gaining weight
Trouble with bowel movements or frequent, greasy stool
Skin that tastes very salty
CAUSES
Caused by a change, or mutation, in a gene called Cystic fibrosis transmembrane conductance regulate
PATHOPHYSIOLOGY
The CFTR protein produced by this gene regulates the movement
Of chloride and sodium ions across epithelial cell membranes
Caused by a mutation in the CFTR
PHARMACOLOGICAL MANAGEMENT
Bronchodilators
Mucus thinners
Anti-inflammatory medicines
CFTR modulators
Antibiotics
Chest therapy or percussion
NURSING CARE PLAN
Administer pain medicine
Provide oxygen musk
Assess cough for effectiveness
Assess the skin colour
Monitor respiratory and heart rate for any changes
REFERENCES
Ahmed, M.I, Mukherjee, S, Treatment for chronic methicillin-sensitive S aureus pulmonary infection in people with cystic fibrosis, Cochrane Database of Systematic Reviews, 3, CD011581,2016
AL-Yateem, N, Child to adult:transitional care for young adults with cystic fibrosis, British Journal of Nursing, 21, 850-4, 2012
