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Systemic inflammatory conditions - Coggle Diagram
Systemic inflammatory conditions
Systemic lupus erythematosus (SLE)
rare in children
most commonly in adolescent females
malaise, arthralgia, malar rash (often photosensitive)
comp = organ involvement
kidneys
haematuria + proteinuria = indications for renal bx
lung
CNS
commoner in Asians + Afro-Caribbeans
C3+4 complement proteins may be low
tx = immunosuppression (intensity depends on severity of renal involvement)
If a pregnant woman has SLE...
a/w recurrent miscarriage, IUGR, pre-eclampsia, placental abruption, PTB
anti Ro + anti La abs can be passed onto baby + cause neonatal lupus syndrome
self limiting rash
rarely heart block
Juvenile Dermatomyositis (JDMS)
rare
usually begins insidiously
facial rash (erythema over bridge of nose + malar areas), voilaceous (heliotropic) doscoloration of eyelids
malaise, progressive weakness, muscle pain
skin over metacarpal + proximal interphalangeal joints may be hypertrophied + pink
nailfold capills may be dilated + tortuous
arthritis in 30%
comps = resp failure + aspiration pneumonia - may be life threatening