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Cystic Fibrosis - Coggle Diagram

- - - - Due to newborn testing
- - - - Cystic fibrosis transmembrane conductance regulator (CTFR modulators)
        
        Combination of 3 medications that improve tthe functio of the faulty CTFR modulator.
        
        Improves lung function and weight
        
        Reduces the amount of salt in sweat
    - - Prevent lung infections
        
        Penicillins
        
        Amoxicillin
        
        Dicloxacillin
        
        Adverse Effects: Nausea, vomiting, diarrhea, black hairy tongue
        
        Cephalosporins
        
        Cephalexin, cefdinir, Cefuroxime
        
        Adverse Effects: Nausea, vomiting, diarrhea, yeast infection
    - - Lessen the swelling in the airways in your lungs
    - - Helps you cough up the mucus which can improve lung function
      - Hypertonic Saline
      - Adverse Effects: Increased cough, sore throat, chest tightness
    - - Help to keep the airway open by relaxing the muscles around the bronchial tubes
      - Ventolin®, ProAir®, Proventil®
      - Adverse Effects: Tremor, nausea, palpitations, nervousness
    - - Help the digestive tract absorb nutrients
    - - Prevent constipation and bowel obstruction
        
        Miralax, Ducalax
        
        Adverse Effects: Diarrhea, pounding heart beat, nausea, vomit
    - - INC. ability of pancreatic enzymes
      - Tums, Milk of magnesia, Pepto-bismol
      - Adverse Effects: Lessens effects of other medications, constipation, gas
  - - - Vest Therapy
        
        Machine that passes air into the lungs
      - Clapping with cupped hands on the front and back of the chest
      - Certain breathing and coughing techniques can help to loosen the mucus.
  - - - Removal of nasal polyps that obstruct breathing
    - - CF interferes with digestion so a FT may be necessary to deliver adequate nutrition
    - - Both lungs need to be replaced.
- - - - Chloride and water are not transported correctly across epithelial membranes
        
        Thick, dehydrated, hypersecretion of mucus
        
        Impaired Mucus clearance of the lungs
        
        chronic bacterial infection: Due to stagnant mucus
        
        chronic neutrophilic inflammation
        
        Bronchiectasis
        
        1 more item...
        
        Thickened pancreatic :enzymes
- - - - Exposure to P. aeruginosa
        
        Rural areas without as much access to water are at a higher risk of obtaining this bacteria.
- - - - Blood sample taken from baby's heel in the first few days after birth.
        
        Places on a "Guthrie Card" where the laboratory will test the blood and look for abnormalities.
  - - - Both arms are covered with a band that makes the baby sweat. The sweat is collected and then reviewed and measured for chloride.
        
        Abnormally high Chloride levels are associated with CF
  - - - If two carriers have a child:
        
        25% chance the child will have CF
        
        50% the child will be a carrier but not have CF
        
        25% chance the child will not be a carrier, not have CF.