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CYSTIC FIBROSIS Mind Map 2 - Coggle Diagram
CYSTIC FIBROSIS
Mind Map 2
Blue Hat
How is it Managed?
Hospitalisation for
Exacerbations
Lung Transplant
Antibiotic Therapy
Physiotherapy
Humidification (Airvo)
Manual Techniques (Percs & Vibes, Assisted autogenic drainage, postural drainage) +/- BiPAP
PEP (Acapella, Aerobika, Flutter, Pari) 5 sec expiration, 8-10 breaths, 8-10 sets
Inhalation therapy (saline, hypertonic saline; 3% or 6%)
Exercise (strength + Aerobic)
Supplemental O2 if spO2 <88%
Supplemental O2 will get improvements in training benefits, not just spO2
Precaution! Remember to replace salts!
Continence/pelvic floor training
Outcome Measures to Monitor
Lung Function & Exercise
Spirometry Testing
6MWT
3 Min step test
Modified shuttle test
Infection Control
People with transmissible Pseudomonas aeruginosa or Burkholderia cepacia complex infection separate from people who do not
Microbiological surveillance
Educate on risk of cross-infection
Enteral tube feeding
Who is involved?
Physiotherapists
Nurses
Doctors
Dieticians
Resp physicians
Clinical psychologists
Pharmacists
Home
Nutrition
Enteral tube feeding
Pancreatic enzyme
replacement therapy
Exercise
Airway clearance
What Happens?
White Hat
Underweight
Fat-soluble vitamin deficiencies
Male infertility, reduced female fertility
Respiratory
Progressive lung disease
Thick, viscous secretions &
Impaired mucociliary clearance
Repetitive inflammatory cycle
Chronic liver disease
Urinary stress incontinence
CF related diabetes
Psychological
Low self-esteem
Anxiety
Body image
Who does it affect?
1 in every 2500 Australian
babies (male or female)
Sweat testing
Heal prick test
Antenatal screeing
Black Hat
Risks/Difficulties with
Treatment
Death
Life expectancy average is 42 years old
Physiotherapy Adverse Events
Pneumothorax
(No PEP, reduce intensity)
Haemoptysis
Cease manual techniques, minimise coughing
Seek medical review
Adherence to program as patients get older
Power struggle with parents
Young adults - smoking, drinking
Balancing work and health
Psychological
Anxiety
low self esteem
body image
What is it?
Chronic Disease
Genetic Mutation
Ideas for
Future Research
Long term effects of chest physiotherapy for CF population
(limited due to ethical considerations)