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Sarcoidosis (Investigations (Chest X-ray: bilateral hilar lymphadenopathy,…
Sarcoidosis
Investigations
Chest X-ray: bilateral hilar lymphadenopathy, peripheral pulmonary infiltrates, fibrosis, honeycombing
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Tissue biopsy of lungs + lymph nodes: diagnostic, shows non caseating granulomata
Bloods: raised ESR, raised LFTs, raised calcium, lymphopenia
Bronchoalveolar lavage: raised lymphocytes in active disease + raised neutrophils with pulmonary fibrosis
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Differential Diagnoses
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Vasculitis: GCA, PN, Wegener's etc
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Pathophysiology
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Biopsies show infiltration of alveolar walls and interstitial spaces with mononuclear cells before granuloma formation
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Typical sarcoid granuloma = focal accumulation of epithelioid cells, macrophages and lymphocytes
Treatment
Oral prednisolone for: parenchymal lung disease, uveitis, hypercalcaemia, neurological + cardiac involvement
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Acute sarcoidosis: bed rest, NSAIDs
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Signs
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Non-Pulmonary
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Hypercalcaemia, hypercalciuria, renal stones
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Definition
Multi-system granulomatous disorder of unknown cause. Non-caseating granulomas form in effected organ tissue
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