Please enable JavaScript.
Coggle requires JavaScript to display documents.
Pulmonary stenosis in children (Diagnosis (History (DH Meds, allergies,…
Pulmonary stenosis
in children
Definition
Congenital disorder where
the pulmonary valve is fused
Epidemiology
Rare
Pathophysiology
Defect
Pulmonary valve leaflets partially fused
Mechanism
Restrictive exit from RV
Reduced blood flow into pulmonary circulation
Backpressure into RV and RVH
Clinical
presentation
Asymptomatic
Cyanosis
(only if duct dependent)
Diagnosis
Examination
Cardio
Thrill, may have RV heave
Murmur (ejection systolic, ULSE)
Investigation
Bloods
Cap blood glucose
FBC, U+E, LFT
Imaging
CXR: normal, post-stenotic
dilatation of pulmonary artery
ECHO: diagnostic
Bedside
Obs
ECG (RVH)
History
DH
Meds, allergies
FH
Heart disorders
Cosanguinuity
PMH
Growth and development
Vaccinations
Known medical conditions
POH
Antenatal: bloods, scans, growth
Perinatal: gestation, delivery, weight
Postnatal: growth, complications
PC/HPC
Asymptomatic, cyanosis
SH
Living arrangements
School and nursery
Management
Surgical
Valvoplasty
Indication: increased RV pressure
MOA: catheter balloon dilatation
Conservative
Information, advice, support
Paeds/cardio referral
Complications
Heart failure
Screening
Antenatal screening programme
Foetal anomaly scan
Neonatal examination
Murmur