Please enable JavaScript.
Coggle requires JavaScript to display documents.
Sturge-Weber
syndrome (Clinical
presentation (Port wine stain
CN V…
Sturge-Weber
syndrome
-
-
Pathophysiology
-
Mechanism
Haemangioma in CN V distribution with associated intracranial lesion (ipsilateral leptomeningeal angioma)
Varied severity; may have epilepsy, intellectual disability and contralateral hemiplegia
Vascular compromise causes epilepsy in developing brain
Clinical
presentation
Port wine stain
CN V distribution
-
-
-
Diagnosis
Examination
-
Neuro exam
Any seizures, hemiplegia
-
-
History
-
-
POH
Scans, bloods, growth, gestation,
delivery, weight, complications
FH
Neurological conditions, port wine stains
PC/HPC
Red facial rash, seizures,
developmental delay
SH
Living arrangements, school/nursery
Management
-
Conservative
Information, advice, support
Medical
Laser tx
Indication: port-wine stain
MOA: destroys vessels,
lightens facial plethora
-