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Coats disease - Coggle Diagram
Coats disease
Treatment
Observation:
Non-vision threatening
Total RD (no hope)
Anti-VEGF
Laser:
For progressive exudation
Multi repeated sessions
Cryotherapy:
Double freeze-thaw
! Increase leakage
Vitreoretinal Sx:
Significant tractional fibrosis
Total exudative RD -> prevent NVG
Enucleation
Complications
Rubeosis iridis
Glaucoma
Uveitis
Cataract
Phthisis bulbi
Epidermiology
75% male
95% unilateral
Age: 1st decade: avg 5 years
Symptoms
Unilateral visual loss
Strabismus
Leucocoria
DDx:
Retinoblastoma
Signs
Telangectasia
Inferior temporal quadrant
Focal aneurysmal arteriolar dilatations
Intra subretinal exudate
Remote from telangectasia
Freq macula involved
Different diagnosis
Familial exudative vitreoretinopathy
ROP
Retinal hemangiomas
Imaging
OCT: macula assessment
FA
Hyperfluorescence
:
Telangectasia
Aneurysmal dilatations
Leakage