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ectodermal dy is (1) splasia - Coggle Diagram
ectodermal dy
splasia
definition
are a group of hereditary conditions characterized by abnormal hair, teeth, fingernails and toenails, and sweat glands.
Treatment
Dentures or implants
Lifestyle adjustments
Special treatment for hair skin and fingernails
Use artificial tears to prevent drying
Use saline nose spray to prevent debris and infection
Take cooling water for bath to keep normal body temperature
signs and symptoms
hearing problems.
Cleft palate/lip.
Missing fingers or toes (digits).
Respiratory infections due to lack of normal protective secretions of the mouth and nose.
missing teeth
dry skin and eyes
Complications
Seizzures
Brain demage
itching of the whole body
Diagnostic procedures
Genetic testing
Biopsy of the skin
X-ray of teeth and bones
Biopsy of mucus membrane
health education
avoid excessive bathing
drink atleast 8 glases of water daily
avoid over scrubbing, lather gently and pat dry
eat nutritious and well balanced diet
report early any signs of skin infection
pathophysiology
is the abnormal morphogenesis of cutaneous and oral embryonal ectoderm (hair, nails, teeth, eccrine glands). also related to the absence or dysfunction of eccrine and mucous glands.
nursing intervention
discourage scratching and keep clients nails short
use tepid water with prescribed detergent only for bathing
immediately apply prescribed topical application only
administer antihistamine, antibiotics, and analgesics as prescribed
references
Fleckman P and DiGiovanna JJ. “The ichthyoses.” In: Wolff K, Goldsmith LA, et al. Fitzpatrick’s Dermatology in General Medicine (seventh edition). McGraw Hill Medical, New York, 2008:401-424.
James WD, Berger TG, et al. “Genodermatoses and congenital anomalies.” In: James WD, Berger TG, et al. Andrews' Diseases of the Skin, Clinical Dermatology (tenth edition), Elsevier, Canada, 2006:560-1.
