ICHTHYOSIS 
Definition
It is a group of skin disorders characterized by dry, scaly or thickened skin.
Pathophysiology
genetically heterogeneous skin disease caused by mutants involving multiple genetic loci.
Lamellar ichthyosis is a rare autosomal recessive,
Clinical manifestations
dry skin, fissures and flakiness
scaly skin
pain
itching
skin peeling
Treatment
Management
Pharmacological
hydrotherapy
prescription creams and ointments
soaking baths
use of moisturizers
oral medications such as rentoids
Vitamin A -derived medications
Causes
Prevention
Choose moisturizer such as petroleum jelly or one that contains urea or propylene glycol-chemicals that help keep the skin moist.
Apply moisturizer while the skin is still moist after bathing.
Avoid strongly scented and antibacterial soaps.
Complications
Diet
Avacados
brocoli
Fatty/oily fish
blistering
skin allergies
skin infections
overheating
skin dehydration
poor skin care
skin dehydration
heredity
stronlgy scentered soaps
genetic mutations involving multiple genetic loci
Diagnostic tests(mayo clinic)
physical examination of the affected
skin biopsy
low protein diet
nursing Care Plan
Desired outcome
Nursing intervention
problem
Risk for infection
Patient to be free from secondary infection
Encourage the patient to maintain good personal hygiene methods
assess for signs of infection
Administer oral antibiotics as prescribed
Apply topical antibiotics
Nursing care Plan(nurseslabs)
Desired outcome
Nursing intervention
Problem
Impaired skin integrity
Patient maintains optimal skin integrity within limits of the disease, as evidenced by intact skin
identify signs of itching and scratching
Encourage the patient to adopt skin care routines to decrease skin irritation
Encourage the patient to bath or shower with lukewarm water and mild soap or non-soap cleansers
Asses the skin systematically, look for areas of irritant and allergic contact
Apply topical lubricants immediately after bathing
Okulicz (2003)
Okulicz (2003)
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Okulicz (2003)
Okulicz (2003)