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Ehler's-Danlos syndrome Ehlers-Danlos-Syndrome - Coggle Diagram
Ehler's-Danlos syndrome 
Defination
connective tissue disorders that can be inherited and are varied both in how they affect the body and in their genetic causes
Pathophysiology
result in increased fragility of connective tissue with arterial, intestinal, and uterine ruptures and premature death
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vascular form sometimes referred to as type IV, is characterized by a decreased amount of type III collagen
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Diagnostic procedures
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Imaging such as CT scan, MRI, ultrasound
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Clinical manifestation
Overly flexible, loose joints, which causes pain and dislocations
Very soft, stretchy and unusually fragile skin
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Nursing management
Helping devices to offer loading assistance to lower edge joints through ambulation and weight bearing activities
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Hypertensive medications to use when the blood vessels are more fragile to reduce maintaining low blood pressure
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References
Junkiert-Czarnecka A, Pilarska-Deltow M, Bąk A, Heise M, Haus O. New variants in COL5A1 gene among Polish patients with Ehlers-Danlos syndrome: analysis of nine cases. Postepy Dermatol Alergol. 2019 Feb. 36 (1):29-33
Zilocchi M, Macedo TA, Oderich GS et-al.Ehlers-Danlos syndrome: imaging findings. AJR Am J Roentgenol. 2007;189 (3): 712-9