Lecture 67: Bulk Transport (Physiology)

MAJOR TYPE 1
ENDOCYTOSIS 💥

1) Phagocytosis

2) Pinocytosis 🚩

2A) Receptor-Mediated Endocytosis

coated vesicles- proteins coating intracellular surface of endocytosing vesicles

cell eating

Receptor-mediated

internalize large particles

-bacteria
-dead or damaged cells
-asbestos fibers, glass beads, etc.

cell drinking

constitutive (always occurring)

internalize extracellular fluid

constitutive (always occurring)

induced (receptor-mediated)

CLINICAL RELEVANCE ⭐
(Phagocytosis)

2B)MACROPINOCYTOSIS
("large cell drinking") 🍾

MAJOR TYPE 2
EXOCYTOSIS 🏴

SNAREs 🏴

Tethering vs. Fusion 🏴

Regulation 🏴
(Examples)

Possible Disease Connections 🏴 ‼

MAJOR TYPE 3
TRANSCYTOSIS 🚩

Energy-dependent

Vesicles <250 nm diameter

Mammalian phagocytic cells

macrophages
dendritic cells
neutrophils

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Induced process (initiated by ligand binding to receptors on phagocytic cells)

Actin cytoskeleton required for internalization!

Phagosomes fuse w/lysosomes to degrade contents/kill bacteria!

Live animal cells

"do not eat me!" signals

membrane proteins that bind to inhibitory receptors on phagocytic cells

early line of defense against bacteria!

Some bacteria have protection mechanisms that allow to escape degradation through phagocytosis!

Salmonella enterica
(food poisoning)

Mycobacteria
(TB)

blocks uncoating of coat proteins that's requires for lysosomal fusion!

secretes protein that blocks fusion of phagosome w/lysosomes -> blocks degradation!

NO degradation of phagocytosed bacteria

live in protected intracellular vesicular environment

Types of Pinocytosis

  1. Clathrin-mediated endocytosis
  1. Caveolin-Coated Vesicle-mediated Endocytosis
  1. Non-clathrin/non-caveolin-mediated endocytosis 🚫

large membrane ruffles fold over to engulf fluid & contents

Actin cytoskeleton involved

blocked by P21-activated kinase-1 (regulates actin dynamics & block/inhibits actin polymerization!)

Pinosomes fuse w/early endosomal compt.

Some viruses use this to enter cell!

vaccinia virus

HIV1

Echovirus type 1

Adenovirus 3

Energy- DEPENDENT!

Constitutive internalization of coated vesicles from plasma membrane

ligand binding to cell surface receptor accelerates int. rate

Coat proteins

"coat" cytoplasmic membrane surface

Types
-clathrin
-caveolin
-others

Basal internalization rate VARIES by cell type!

Macrophages internalize ~3% of membrane SA/minute
Fibroblasts ~1%/minute

accelerated by GF/hormone binding

Total plasma membrane SA NOT changed, so equivalent amounts of plasma membrane are being internalized & replaced

MANY viruses use this pathway for mammalian cell entry!

Examples
-Hepatitic C virus
-Dengue virus
-Reovirus

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distinct membrane lipid & protein composition (cholesterol & sphingolipid-rich)

form signaling membrane subdomains

dynamin-2-dependent (pinching off similar to clathrin-coated vesicles)

regulated by src Family Kinases

MULTIPLE TYPES! Caveolin 1,2, 3

Caveolin 1 & 2
(expressed by most cells)

Caveolin 3= Unique!
-only expressed in skeletal/smooth mm., glial cells, early post-natal peripheral nn.

Pathologies

Viruses using caveolin-coated vesicle entry pathway

SV40 virus

papillomarvirus

diseases assoc. w/Caveolin 3 mutations

limb girdle musc. dystrophy

rippling muscle disease

distal myopathy

hyperCKemia

LDL Receptor Recycling & Disease 🔥

Specific plasma membrane LDL (low-density lipoprotein) receptors

LDL receptors w/bound LDL cluster in clathrin-coated pits

LDL interalized more SLOWLY in the absence of LDL receptors

receptors w/bound LDL internalized FASTER (than those without)

LDL internalization downregulate cholesterol synthesis

Hypercholesterolemia

caused by:
-LDL receptor deficiency
-LDL receptor mutation inhibiting localization to clathrin-coated pits

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Notice: xanthomas arise from deposition of plasma LDL-derived cholesterol into macrophages of skin

coat protein(s)-if any- & mechanism is UNKNOWN!

Viruses using pathway:
-Rotavirus
-Influenza virus
-Lymphocytic choriomeningitis virus

energy-dependent! (ATP)

"priming" of membrane site for vesicle fusion to occur

exocyst complex

secures secretory vesicle to plasma membrane

Types of Processes!

Constitutive

Regulated

continuous
Ca2+ dependent!

respond to signal (ligand binding to membrane receptor, ex: NT release)

Ca2+ dependent!

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Soluble NSF (NEM-Sensitive Factor) Activating Protein Receptor Protein

at least 39 different SNAREs identified!

2 Basic Types

1) v-SNARE

2) t-SNARE

vesicle-SNARE

target-SNARE

mediate vesicle fusion

Ca2+ dependent self-assembly forms conducting channels spanning 2 lipid bilayers -> brings them VERY CLOSE together!

Exocyst complex
Tethering
v-SNARE/t-SNARE
Fusion! ⭐

different v/t-SNARE combo's impact specificity of vesicle fusion events!

Tethering Vesicles to target membrane mediated by "tethers" (Rab effector proteins)- small G-protein ❗

Homotypic Tethering

Heterotypic Tethering

2 intracellular vesicles fuse!

fusion of 1 intracellular vesicle + plasma membrane

Fusion of exocytic vesicle w/plasma membrane (mediated by SNAREs)

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Secretion of Growth factor(s) like NT's from neurons

Insertion of membrane transporters (regulate transport activity)

1) Synaptic Exocytosis Defects 🏁

2) Type 2 Diabetes 🏁

3) Cystic Fibrosis (CF) 🏁

may play role in multiple neurodegenerative diseases

some types assoc. w/diminished depolarization-induced insulin exocytosis

some CFTR mutations impede movement by vesicles from ER -> plasma membrane

Endocytosis of fluid & solutes along with receptor-bound ligands from 1 solution (apical or basolateral)

movement within vesicles through cell

exocytosis of vesicle contents at other membrane surface

COMBO of endocytosis (1 side) and EXO (other side)!

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Examples:
-Endothelia & capillaries
-Intestinal epithelia
-Lung
-Thyroid
-BBB