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Bleeding and coagulation disorders (Von Willebrand disease (What deficient…
Bleeding and coagulation disorders
Hereditary haemorrhagic telangiectasia
Diagnosis criteria
Autosomal link
Immune Thrombocytopenic Purpura
Presentation kids
Thrombotic thrombocytopenia purpura
Presentation
Gene
Haemophilia A
Deficient in
Features
Compared to VWd
PTT and PT
Haemophilia B
Factor deficient
Features
PTT and PT
Von Willebrand disease
What deficient in
Type 1, 2, 3
Diagnosis
Features (compared to Haemophilia)
Disseminated intravascular coagulation
Features
Especially diagnostic of DIC
Causes
Diagnosis
Vitamin K
Diagnosis
Factors needed
Antithrombin deficiency
Features
Factor V leiden
Deficient in what
Epidemiology
Risk of VTE
Protein C/S deficiency
Deficient in what
Risk of VTE
Antiphospholipid syndrome
Features
Diagnosis