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Muscular Dystrophy (Pathophysiology (Normal respiratory function, Adequate…
Muscular Dystrophy
Etiology
X-linked recessive trait disorder that occurs almost exclusively in males
Pathophysiology
Normal respiratory function
Adequate Ventilation but ineffective cough
Adequate daytime ventilation but inadequate nighttime ventilation
Inadequate ventilation during daytime AND nighttime
Clinical Signs & Symptoms
Muscle Pain and weakness
Flaccid Muscles
Cardiopulmonary failure
Diagnostic Tests
Genetic Testing
Absence of the dystrophin protein in protein analysis of muscle tissue
ECG showing inverted T waves and PFT showing decreased values
Respiratory Management
Oxygen Support
Bronchial Hygiene
Lung expansion
Trach/intubate as needed/ABG showing resp failure
Differential Diagnosis
Guillain Barre
Myasthenia Gravis
Tetanus