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Antiphospholipid Syndrome (Features (Venous/Arterial Thrombosis, Recurrent…
Antiphospholipid Syndrome
Definition
Acquired autoimmune hypercoagulable state caused by antiphospholipid antibodies provoking arterial/VTE, reccurent pregnancy loss and thrombocytopaenia
Aetiology
SLE
Other autoimmune disorders
Lymphoproliferative disorders
Phenothiazines
Features
Venous/Arterial Thrombosis
Recurrent foetal loss
Thrombocytopaenia
Paradoxical rise in APTT
Livedo Reticularis
Pulm HTN and Pre-eclampsia
Investigations
Coag
Screen for other clotting abnormalities
Treatment
Initial VTE
Warfarin (2-3) for 6/12
Recurrent VTE
Lifelong Warfarin
If occured while taking, increased target 3-4
Arterial TE
Lifelong warfarin (2-3)