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restrictive lung diseases (occupational (Coal dust: pneumoconiosis,…
restrictive lung diseases
pulmonary infiltration esinophilia
simple
diffuse alveolar damage, alveolar interstitial infiltration.
prolonged
worms are indicated
aspergillus fumigatus
allergic broncho-pulmonary aspergillosis
-> bronchiectasis -> progressive pulmpnary fibrosis -> mucoid impaction =collapse of lung,
aspergiloma
ball of mycelium,
invasive aspergilosis.
usually immuno compromised pt.
occupational
NH4, sulfur dioxide, Cl, or oxides of nitrogen
: Acute bronchitis, pulmonary edema,
mineral dust
: pulmonary fibrosis
Occupational asthma: common
microbial spores and vegetable matter
: extrinsic allergic alveolitis
Asbestos, polycyclic hydrocarbons, radon in mines.
: bronchial carcinoma, extensive fibrosis resembling PIF and disability.
iron
siderosis
barium
: baritosis
tin
stannosis
Coal dust
: pneumoconiosis, immediate fibrogenic effect.
progressive massive fibrosis
Quarts
: silicosis: fibrogenic,
progressive massive fibrosis
granulomatous
CT diseases Resp manifestations:
RA, SLE, systemic sclerosis
hypersensitivity pneumonitis
chronic form produces granuloma which distinguishes it from IPF.
anti-neutrophil-cytoplasmic antibodies (ANCA) microscopic polyantitis
-
wegeners granulomatosis (granulomatosis with polyangitis), churg-straus disease (esinophilic granulomatosis with poly angitis)
Sarcoidosis
non-necrotising granulomas along brinchvascular branches and lobular fissures.
goodpastures and idiopathic pulmonary haemosiderosis
Good pastures syndrome
due to type 2 cytotoxic reaction, involved the kidney and lungs
idiopathic pulmonary haemosiderosis
similar yet no basement membrane antibodies in serum and haemosiderin laden macrophages in sputum.
pulmonary fibrosis
"honeycomb lung"
Localised
, e.g after unresolved pneumonia
bilateral
: e.g. TB
Widespread
: IPF
idiopathic pulmonary fibrosis
dust, wood, or auto immunity. organising diffuse alveolar damage.
Rare ones
pulmonary alveolar protinosis
, different from extrinsic allergic alveolitis by INSPIRATORY crackles.
extrinsic allergic alveolitis
also known as farmers lung, bird poo.
Clinical features of respiratory lung diseases
Dysopnea
Cyanosis
pulmonary hypertension ->Cor-pulmonale
Resp failure
examination:
finger clubbing, fin crackles usually bilaterally
investigations
CXR: usually ground glass appearance , progressing to nodular shadows and then honeycomb appearance.