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Cystic Fibrosis (Adolescent (DM, Cirrhosis & portal HT, Pneumothorax…
Cystic Fibrosis
Adolescent
DM
Cirrhosis & portal HT
Pneumothorax & recurrent Haemoptysis
Distal Intestinal Obstruction
Asperglosis "ABPA"
Sterility in Males
Young Child
Nasal Polyp
Bronchiectasis
Sinusitis
Rectal Prolapse
Infant
Recurrent Chest infection
Malabsorption + Steatorrhae
Failure to thrive
Meconium illeus
MC Bacterial causes
Burkholderia species
Staph aureus
Psuedmonas areginosa
H. Infleunza
Dx
10–40 mmol/L normal
Cl 60–125 mmol/L in cystic fibrosis
Sweat test
Using Pilocarpine Iontophoresis
NewBorn
Dx thru newborn screening
Gluthrie Test
Prolong neonatal Jaundice