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Scleroderma (Diffuse Scleroderma (Raynaud's, Puffy or hidebound skin,…
Scleroderma
Diffuse Scleroderma
Raynaud's
Puffy or hidebound skin
Truncal + acral involvement
Nailfold capillary
(+) Anti-Scl70
(+) anti-RNA polymerase
Dermatomyositis
Heliotrope Rash over eyelids
Gottrons Papules: MCP, PIP, MTP, knees, elbows
V-neck rash
Periungual erythema
Calcinosis
HIGH risk of malignancy
Limited Scleroderma
Raynaud's
Acral distribution
nailfold capillary pattern
Pulmonary HTN
(+) ACA
Features
Raynaud's
Smooth facial features
Telangiectasias
Dilated capillary loops at nail bed
Treatment
GI reflux
PPIs
Raynaud
CCBs
Hypertensive renal crisis
ACEI
Captopril
Pulmonary HTN
Bosantan