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SLE (Systemic Lupus Erythematosus) (Concepts (Systemic - every organs,…
SLE
(Systemic
Lupus
Erythematosus)
Concepts
Immunologic
Autoimmune
Attack self
Systemic -
every organs
Alopecia
Skin rash
Joint
Multiorgan
Involved
Heart, lungs, kidneys
Hematologic
Muscle pain
General
Fatigue, Fever
Rash
What we see
on Face
Malar rash
Inflammation
Phenomenon
Pathophysiologic
Lupus
Wolf’s bite
13th century,
Dr. Rogerius
Erosive
facial lesions
Labs
ANTIbody
Specific
Ds-DNA
Anti-SM
Sensitive
ANA
Routine
Complement3,4
Decreased
Pancytopenia
CBC
Kidney
Cr
UA
w/ microscopy
Muscle
CPK
inflammation
CXR
Lungs
ESR
Tx
Class
Immune-modulating
Cyclo-sporine A
Cyclo-phosphamide
Azathioprine
Rituximab
Anti-inflammatory
Anti-malarial
NSAIDs
Corticosteroids
Methotrexate
Mild
Cutaneous sx
Serositis
MSK symptoms
NSAIDS
Hydroxy-chloroquine
Short course steriods
Severe
High dose steroids
Immunosuppressive
Cyclophosphamide(reserved d/t toxicity),
azathioprine,
mycophenolate
Rituximab
Organ (Lupus nephritis)
Criteria
(ACR)
:1234: 4 out of 11
D.O.P.A.M.I.NE
R.A.S.H.
DIscoid rash
Oral ulcer
Photosensitivity
Arthritis : Nonerosive
Malar rash
Immunologic (+) - dsDNA, Sm, false + syphilis
Neurologic (sz, psychosis)
Renal disorder (ptnuria, hematuria, glumerulonephritis)
ANA +
Serositis
Hematologic
Sensitivity 85
specificity 95
REHAB
Education
To prevent skin breakdown
Aerobic Exercise
As
Fatigue
:!: is
Main limiting factor for ADL
Energy
Conservation
Technique
protect
joints
by doing jobs efficiently
HOW?
Planning
ahead.
In a
sequential
way.